Publication Date

5-1-2023

Journal

The Texas Heart Journal

DOI

10.14503/THIJ-22-7974

PMID

37268281

Publication Date(s)

May 2023

Language

English

PMCID

PMC10353275

PubMedCentral® Posted Date

5-26-2023

PubMedCentral® Full Text Version

Post-Print

Published Open-Access

yes

Keywords

Adolescent, Female, Humans, Atrial Fibrillation, Tachycardia, Ventricular, Anti-Arrhythmia Agents, Treatment Outcome, Defibrillators, Implantable

Abstract

Catecholaminergic polymorphic ventricular tachycardia is a rare but lethal heritable arrhythmia syndrome associated with both atrial and ventricular arrhythmias. Treatment includes antiarrhythmics, sympathetic denervation, and implantable cardioverter-defibrillators. The use of atrioventricular nodal ablation as a treatment strategy to prevent ventricular arrhythmias in catecholaminergic polymorphic ventricular tachycardia was not found in the literature. This report describes a teenager with a presenting rhythm of atrial and ventricular fibrillation and cardiac arrest. Her clinical arrhythmia was predominantly atrial dysrhythmias, which delayed her diagnosis of catecholaminergic polymorphic ventricular tachycardia. Before her diagnosis, she underwent atrioventricular nodal ablation in an effort to prevent ventricular arrhythmias, which was ultimately ineffective. This report highlights the importance of recognizing atrial arrhythmias in catecholaminergic polymorphic ventricular tachycardia and provides evidence that atrioventricular nodal ablation is not an effective treatment strategy for this disease.

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