A Rare Case of Isolated Thoracic Al-Amyloidoma Causing Complete Atelectasis of the Right Lung

Authors

Smruti Rath
Nicholas Joseph Dcunha
Neel Bhan
Bettye Cox
Muhammad Adrish

Publication Date

1-1-2023

Journal

Respiratory Medicine Case Reports

DOI

10.1016/j.rmcr.2023.101837

PMID

36970497

PMCID

PMC10031536

PubMedCentral® Posted Date

3-13-2023

PubMedCentral® Full Text Version

Post-print

Published Open-Access

yes

Keywords

Amyloidoma, Tumoral amyloidosis, Respiratory failure

Abstract

Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing atelectasis of the right lung. Our case patient had greater morbidity due to late presentation and extensive disease at diagnosis, precluding any surgical intervention. Radiation therapy and medical management were unsuccessful in reducing disease burden. Early diagnosis and detection are pivotal to improving survival in patients with isolated thoracic amyloidoma.