Language
English
Publication Date
8-1-2020
Journal
The Texas Heart Journal
DOI
10.14503/THIJ-16-6094
PMID
33472229
PMCID
PMC7819445
PubMedCentral® Posted Date
8-20-2020
PubMedCentral® Full Text Version
Post-print
Abstract
Platypnea-orthodeoxia syndrome, a rare condition characterized by posture-related dyspnea, is usually caused by an intracardiac shunt, hepatopulmonary syndrome, or shunting resulting from severe pulmonary disease. We report the case of a 33-year-old woman who presented with increasing dyspnea and oxygen desaturation when she sat up or arose. Our diagnosis was platypnea-orthodeoxia syndrome. A lead of a previously implanted pacemaker exacerbated a severe tricuspid regurgitant jet that was directed toward the patient's intra-atrial septum. Percutaneous closure of a small secundum atrial septal defect eliminated right-to-left shunting and substantially improved the patient's functional status. In addition to this case, we discuss this unusual condition.
Keywords
Adult, Cardiac Catheterization, Dyspnea, Echocardiography, Transesophageal, Female, Heart Septal Defects, Atrial, Humans, Hypoxia, Syndrome, Defibrillators, implantable/adverse effects; dyspnea/etiology; heart septal defects, atrial/complications/diagnostic imaging/therapy; hypoxia/etiology; posture/physiology; treatment outcome; tricuspid valve insufficiency/complications
Published Open-Access
yes
Recommended Citation
Borgaonkar, Sanket P; Lam, Wilson W; Razavi, Mehdi; et al., "Platypnea-Orthodeoxia Syndrome Caused by an Intracardiac Shunt" (2020). Faculty and Staff Publications. 975.
https://digitalcommons.library.tmc.edu/baylor_docs/975