Publication Date
5-1-2022
Journal
The Texas Heart Journal
DOI
10.14503/THIJ-20-7393
PMID
35763036
Publication Date(s)
May 2022
Language
English
PMCID
PMC9242634
PubMedCentral® Posted Date
6-28-2022
PubMedCentral® Full Text Version
Post-Print
Published Open-Access
yes
Keywords
Cardiovascular abnormalities, disease-free survival, drainage, heart defects, congenital/diagnosis/surgery, infant, pulmonary veins/abnormalities/diagnostic imaging/surgery, treatment outcome, vascular surgical procedures/methods
Copyright
This work is licensed under a Creative Commons Attribution-NonCommercial-No Derivative Works 4.0 International License.
Abstract
Total anomalous pulmonary venous return is a congenital heart malformation characterized by anomalous pulmonary venous inflow to the right atrium. Surgical repair typically occurs during the first month of life, and survival beyond that age in untreated patients is unlikely. We report an extreme case of supracardiac total anomalous pulmonary venous return in an infant who survived 7 months despite atypical anomalous inflow without atrial-level communication and with right-to-left shunting only through a patent ductus arteriosus. We stabilized the patient's left-sided heart function before surgically repairing the anomalous venous return 2 months later. Three years postoperatively, the patient was well.