Publication Date
8-1-2015
Journal
The Texas Heart Journal
DOI
10.14503/THIJ-14-4352
PMID
26413012
Publication Date(s)
August 2015
Language
English
PMCID
PMC4567122
PubMedCentral® Posted Date
8-1-2015
PubMedCentral® Full Text Version
Post-Print
Published Open-Access
yes
Keywords
Death, Sudden, Cardiac, Defibrillators, Implantable, Electric Countershock, Humans, Patient Selection, Primary Prevention, Prosthesis Design, Risk Assessment, Risk Factors, Transposition of Great Vessels, Treatment Outcome
Copyright
This work is licensed under a Creative Commons Attribution-NonCommercial-No Derivative Works 4.0 International License.
Abstract
Transposition of the great arteries encompasses a set of structural congenital cardiac lesions that has in common ventriculoarterial discordance. Primarily because of advances in medical and surgical care, an increasing number of children born with this anomaly are surviving into adulthood. Depending upon the subtype of lesion or the particular corrective surgery that the patient might have undergone, this group of adult congenital heart disease patients constitutes a relatively new population with unique medical sequelae. Among the more common and difficult to manage are cardiac arrhythmias and other sequelae that can lead to sudden cardiac death. To date, the question of whether implantable cardioverter-defibrillators should be placed in this cohort as a preventive measure to abort sudden death has largely gone unanswered. Therefore, we review the available literature surrounding this issue.