Publication Date
4-1-2019
Journal
The Texas Heart Institute Journal
DOI
10.14503/THIJ-17-6368
PMID
31236081
Publication Date(s)
April 2019
Language
English
PMCID
PMC6555286
PubMedCentral® Posted Date
4-1-2019
PubMedCentral® Full Text Version
Post-Print
Published Open-Access
yes
Keywords
Abnormalities, Multiple, Cardiac Pacing, Artificial, Electrocardiography, Follow-Up Studies, Heart Block, Heart Defects, Congenital, Heart Ventricles, Humans, Infant, Newborn, Male
Copyright
This work is licensed under a Creative Commons Attribution-NonCommercial-No Derivative Works 4.0 International License.
Abstract
Congenital complete heart block with concomitant biventricular noncompaction cardiomyopathy has been reported once previously. Although not universal, when restrictive physiology is present, impaired diastolic filling may pose a distinct challenge to pacing during the neonatal period. We present the case of a neonate with congenital complete heart block and biventricular noncompaction that resulted in severe diastolic dysfunction and atrioventricular dyssynchrony. We intentionally used 2:1 ventricular pacing to provide atrioventricular synchrony with every paced beat, and this resulted in hemodynamic and clinical improvement. This unconventional pacing technique may be beneficial in other neonates who have complete heart block and diastolic dysfunction.