Publication Date
6-1-2019
Journal
The Texas Heart Institute Journal
DOI
10.14503/THIJ-17-6521
PMID
31708710
Publication Date(s)
June 2019
Language
English
PMCID
PMC6827466
PubMedCentral® Posted Date
6-1-2019
PubMedCentral® Full Text Version
Post-Print
Published Open-Access
yes
Keywords
Abnormalities, Multiple, Aorta, Thoracic, Blood Vessel Prosthesis Implantation, Cardiac Catheterization, Computed Tomography Angiography, Coronary Vessel Anomalies, Coronary Vessels, Echocardiography, Female, Fluoroscopy, Humans, Infant, Newborn, Pulmonary Artery, Turner Syndrome
Copyright
This work is licensed under a Creative Commons Attribution-NonCommercial-No Derivative Works 4.0 International License.
Abstract
Anomalous origin of the right coronary artery from the pulmonary artery, a rare congenital cardiac defect, is typically not diagnosed during infancy. On the other hand, Turner syndrome is usually diagnosed early, and it is classically associated with bicuspid aortic valve and aortic coarctation. Individuals with Turner syndrome are also at increased risk for coronary artery anomalies. We present a case of anomalous right coronary artery from the pulmonary artery in a week-old neonate who also had Turner syndrome, patent ductus arteriosus, transverse aortic arch hypoplasia, and impaired ventricular function. Prostaglandin therapy through the ductus increased the patient's myocardial perfusion. Four months after corrective surgery, she was doing well. We discuss the reperfusion phenomenon in our patient's case, as well as other considerations in this combination of congenital defects.