Publication Date

6-1-2019

Journal

The Texas Heart Institute Journal

DOI

10.14503/THIJ-17-6521

PMID

31708710

Publication Date(s)

June 2019

Language

English

PMCID

PMC6827466

PubMedCentral® Posted Date

6-1-2019

PubMedCentral® Full Text Version

Post Print

Published Open-Access

yes

Keywords

Abnormalities, Multiple, Aorta, Thoracic, Blood Vessel Prosthesis Implantation, Cardiac Catheterization, Computed Tomography Angiography, Coronary Vessel Anomalies, Coronary Vessels, Echocardiography, Female, Fluoroscopy, Humans, Infant, Newborn, Pulmonary Artery, Turner Syndrome

Abstract

Anomalous origin of the right coronary artery from the pulmonary artery, a rare congenital cardiac defect, is typically not diagnosed during infancy. On the other hand, Turner syndrome is usually diagnosed early, and it is classically associated with bicuspid aortic valve and aortic coarctation. Individuals with Turner syndrome are also at increased risk for coronary artery anomalies. We present a case of anomalous right coronary artery from the pulmonary artery in a week-old neonate who also had Turner syndrome, patent ductus arteriosus, transverse aortic arch hypoplasia, and impaired ventricular function. Prostaglandin therapy through the ductus increased the patient's myocardial perfusion. Four months after corrective surgery, she was doing well. We discuss the reperfusion phenomenon in our patient's case, as well as other considerations in this combination of congenital defects.

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