Rapunzel Syndrome Complicated By Escherichia Coli Sepsis, Bowel Perforation, and Pancreatitis In An 11-Year-Old Malnourished Female

Authors

Rhea Daniel
Mary Arbuthnot
Srinivas Ramireddy
Supriya Nair

Language

English

Publication Date

2-1-2022

Journal

Journal of Pediatric Gastroenterology and Nutrition

DOI

10.1097/PG9.0000000000000171

PMID

37168751

PMCID

PMC10158331

PubMedCentral® Posted Date

January 2022

PubMedCentral® Full Text Version

Post-print

Abstract

The most common presenting symptoms of Rapunzel syndrome include abdominal pain (37%), nausea and vomiting (33.3%), obstruction (25.9%), and peritonitis (18.3%). Less commonly, patients may present with weight loss (7.4%) or intussusception (7.4%). Exceedingly rare complications of Rapunzel syndrome include gastric ulceration, obstructive jaundice, and acute pancreatitis as well as other malabsorptive-related complications including protein-losing enteropathy, iron deficiency, and megaloblastic anemia. This report details the case of an 11-year-old female with Rapunzel syndrome complicated by sepsis, a rare complication reported in only 2% of patients.

Keywords

Rapunzel syndrome, trichobezoar, sepsis, pancreatitis

Published Open-Access

yes

Recommended Citation

Daniel, Rhea; Arbuthnot, Mary; Ramireddy, Srinivas; et al., "Rapunzel Syndrome Complicated By Escherichia Coli Sepsis, Bowel Perforation, and Pancreatitis In An 11-Year-Old Malnourished Female" (2022). Faculty, Staff and Student Publications. 2270.
https://digitalcommons.library.tmc.edu/uthmed_docs/2270