Faculty, Staff and Student Publications

Publication Date

2-1-2026

Journal

Arteriosclerosis, Thrombosis, and Vascular Biology

DOI

10.1161/ATVBAHA.125.323743

PMID

41410053

PMCID

PMC12922767

PubMedCentral® Posted Date

2-21-2026

PubMedCentral® Full Text Version

Author MSS

Abstract

C1INH (C1-inhibitor) is a multifunctional SERPIN (serine protease inhibitor) that functions as a major negative regulator of the complement, coagulation, and kallikrein-kinin systems. C1INH products were originally developed for the treatment of hereditary angioedema associated with C1INH deficiency. A growing body of literature indicates that C1INH products may find utility in the management of several other disease states. In this review, we detail the key biological activities of C1INH and consider the pathophysiological role of C1INH targets in many conditions. The therapeutic potential of exogenous C1INH is highlighted in the settings of thromboembolism, ischemia-reperfusion injury, sepsis, transplantation, and coronavirus disease 2019.

Keywords

Humans, Complement C1 Inhibitor Protein, Animals, COVID-19, Vascular Diseases, Reperfusion Injury, Blood Coagulation, Sepsis, C1-inhibitor protein, Hereditary Angioedema, Blood Coagulation, Complement, Vascular Diseases

Published Open-Access

yes

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