Faculty, Staff and Student Publications
Language
English
Publication Date
8-2-2025
Journal
Advances in Respiratory Medicine
DOI
10.3390/arm93040027
PMID
40862699
PMCID
PMC12382859
PubMedCentral® Posted Date
8-2-2025
PubMedCentral® Full Text Version
Post-print
Abstract
Primary ciliary dyskinesia (PCD) is a rare, genetically heterogeneous disorder that impairs mucociliary clearance and leads to progressive lung disease. This study aimed to characterize lung function decline in a genetically homogeneous cohort of Puerto Rican patients with
Keywords
Humans, Male, Female, Adult, Retrospective Studies, Middle Aged, Child, Adolescent, Ciliary Motility Disorders, Kartagener Syndrome, Forced Expiratory Volume, Young Adult, Spirometry, Respiratory Function Tests
Published Open-Access
yes
Recommended Citation
Román-Ríos, Gabriel; Rosario-Ortiz, Gabriel; Ramos-Benitez, Marcos J; et al., "RSPH4A-PCDx: An Index to Predict Lung Function Decline in Primary Ciliary Dyskinesia" (2025). Faculty, Staff and Student Publications. 4232.
https://digitalcommons.library.tmc.edu/uthmed_docs/4232
Comments
This article has been corrected. See Adv Respir Med. 2025 Oct 15;93(5):45.