Faculty, Staff and Student Publications

Publication Date

1-1-2022

Journal

Frontiers in Cell and Developmental Biology

DOI

10.3389/fcell.2022.931387

PMID

36051438

PMCID

PMC9424994

PubMedCentral® Posted Date

8-16-2022

PubMedCentral® Full Text Version

Post-print

Abstract

Glioblastoma (GBM) is a high-grade, aggressive brain tumor with dismal median survival time of 15 months. Chromosome 6q (Ch6q) is a hotspot of genomic alterations, which is commonly deleted or hyper-methylated in GBM. Two neighboring genes in this region, QKI and PRKN have been appointed as tumor suppressors in GBM. While a genetically modified mouse model (GEMM) of GBM has been successfully generated with Qk deletion in the central nervous system (CNS), in vivo genetic evidence supporting the tumor suppressor function of Prkn has not been established. In the present study, we generated a mouse model with Prkn-null allele and conditional Trp53 and Pten deletions in the neural stem cells (NSCs) and compared the tumorigenicity of this model to our previous GBM model with Qk deletion within the same system. We find that Qk but not Prkn is the potent tumor suppressor in the frequently altered Ch6q region in GBM.

Keywords

GBM, parkin, QKI, glioma, glioblastoma

Published Open-Access

yes

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